Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease covers the broad medical problems and specific pulmonary conditions in patients with pediatric neuromuscular disease, ranging from the different types of neuromuscular disease, their pathophysiology, and assessment and management, including both novel disease modifying pharmacotherapies and state-of-the-art clinical management. This book provides evidence-based guidance for pediatric patients with neuromuscular disease, and is a valuable resource to pediatric pulmonologists, critical care physicians, and respiratory therapists who want an update and understanding on the cutting-edge therapies and standards of care for managing this population.
1. Section 1: Introduction - p. xiv 2. Chapter 1. Types of neuromuscular disease - p. 3 3. Chapter 2. Pulmonary pathophysiology of neuromuscular disease - p. 23 4. Chapter 3. The natural history of pulmonary disease - p. 37 5. Section 2: Assessment - p. 42 6. Chapter 4. Assessment of pulmonary function - p. 45 7. Chapter 5. Assessment of sleep-disordered breathing - p. 59 8. Chapter 6. Assessment of need for airway clearance - p. 73 9. Section 3: Clinical management - p. 78 10. Chapter 7. Disease-modifying pharmacotherapies - p. 81 11. Chapter 8. Airway clearance - p. 91 12. Chapter 9. Aerodigestive problems and management in children with neuromuscular disorders - p. 111 13. Chapter 10. Chronic mechanical ventilation - p. 125 14. Chapter 11. Thoraco-spinal disease - p. 149 15. Chapter 12. Challenges in managing hypertonic neuromuscular disease - p. 161 16. Chapter 13. Management of acute respiratory failure in neuromuscular disease - p. 171 17. Chapter 14. Home management - p. 191 18. Section 4: Patient focused - p. 204 19. Chapter 15. Transition from pediatric to adult care in neuromuscular disease - p. 207 20. Section 5: Conclusion - p. 216 21. Chapter 16. The evolving course of neuromuscular disease - p. 219 22. Index - p. 233
Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease covers the broad medical problems and specific pulmonary conditions in patients with pediatric neuromuscular disease, ranging from the different types of neuromuscular disease, their pathophysiology, and assessment and management, including both novel disease modifying pharmacotherapies and state-of-the-art clinical management. This book provides evidence-based guidance for pediatric patients with neuromuscular disease, and is a valuable resource to pediatric pulmonologists, critical care physicians, and respiratory therapists who want an update and understanding on the cutting-edge therapies and standards of care for managing this population.
1. Section 1: Introduction - p. xiv 2. Chapter 1. Types of neuromuscular disease - p. 3 3. Chapter 2. Pulmonary pathophysiology of neuromuscular disease - p. 23 4. Chapter 3. The natural history of pulmonary disease - p. 37 5. Section 2: Assessment - p. 42 6. Chapter 4. Assessment of pulmonary function - p. 45 7. Chapter 5. Assessment of sleep-disordered breathing - p. 59 8. Chapter 6. Assessment of need for airway clearance - p. 73 9. Section 3: Clinical management - p. 78 10. Chapter 7. Disease-modifying pharmacotherapies - p. 81 11. Chapter 8. Airway clearance - p. 91 12. Chapter 9. Aerodigestive problems and management in children with neuromuscular disorders - p. 111 13. Chapter 10. Chronic mechanical ventilation - p. 125 14. Chapter 11. Thoraco-spinal disease - p. 149 15. Chapter 12. Challenges in managing hypertonic neuromuscular disease - p. 161 16. Chapter 13. Management of acute respiratory failure in neuromuscular disease - p. 171 17. Chapter 14. Home management - p. 191 18. Section 4: Patient focused - p. 204 19. Chapter 15. Transition from pediatric to adult care in neuromuscular disease - p. 207 20. Section 5: Conclusion - p. 216 21. Chapter 16. The evolving course of neuromuscular disease - p. 219 22. Index - p. 233